 Five- and 10-year survival rates in patients treated with IVIG were 91% and 77%, respectively, compared to 47% and 37% in patients not treated with IVIG.Moreover, better identification and management of this condition appears to be resulting in lower mortality and improving survival and quality-of-life results as of late.The syndrome was first described by a team of New York City physicians led by Dr. Bayard D. Clarkson in 1960, after whom it was later informally named.