 In general, 80–99% of individuals exhibit malabsorption of fats and fat-soluble vitamins.Approximately 30%-79% of people with the disease display symptoms of abnormality of the retinal pigmentation, ataxia, muscular hypotonia or reduced tendon reflexes.The signs and symptoms of Abetalipoproteinemia appear in the first few months of life (because pancreatic lipase is not active in this period).