 The prevalence of DE ranges from 0.06% to 7.7% depending on the race.It is more common in men than in women, more frequent in the mandibular teeth than the maxillary teeth.Patients with Ellis-van Creveld syndrome, incontinentia pigmentiachromians, Mohr syndrome, Rubinstein-Taybi syndrome and Sturge Weber syndrome are at a higher risk of having DE.