It is produced by the transamination of an alpha-keto acid and along with tyrosine is one of the end products of the prephenate branch from chorismate.
It is produced by the transamination of an alpha-keto acid and along with tyrosine is one of the end products of the prephenate branch from chorismate. Both it and tyrosine are degraded by oxygenases to acetoacetate and fumarate during the urea cycle. In the event of an absence of its hydroxylase, it accumulates in bodily fluids, and if untreated can lead to severe mental retardation and death. FTP, identify this amino acid the deficiency of which is autosomal recessive and which is present in many sodas.
It is produced by the transamination of an alpha-keto acid and along with tyrosine is one of the end products of the prephenate branch from chorismate.
phenylalanine