Defective versions of these can result in RCPD, AMN, and X-linked adrenoleukodystrophy. Another defect results in the inability to metabolize phytanic acid, a condition known 
Defective versions of these can result in RCPD, AMN, and X-linked adrenoleukodystrophy. Another defect results in the inability to metabolize phytanic acid, a condition known as Refsum disease, and it is also the location where plasmalogen synthesis begins. Some proteins being targeted to this organelle rely on a string of serine-lysine-leucine residues at the C-terminus, the SLK sequence. Those amino acids bind to PTSR receptors, defects in which can cause Zellweger syndrome. Fatty acids are oxidized to acetyl CoA here, though it is best known for the enzyme catalase. For 10 points, name this organelle that isolates and degrades toxic peroxide species.
Defective versions of these can result in RCPD, AMN, and X-linked adrenoleukodystrophy.
peroxisomes