For 10 points, name this disease caused by a defective chloride ion transporter which affects the lungs and pancreas.
Lumacaftor and ivacaftor are two drugs designed to treat forms of this disease with different genetic aetiologies. This disease is the most common cause of distal intestinal obstruction syndrome and the related meconium ileus. The genetic mutations that cause this disease are also the most common cause of congenital absence of the vas deferens. Another effect of this disease is increased salinity of sweat, which can form the basis of a diagnostic test. For 10 points, name this disease caused by a defective chloride ion transporter which affects the lungs and pancreas.
Lumacaftor and ivacaftor are two drugs designed to treat forms of this disease with different genetic aetiologies.
{Cystic fibrosis}