Von Gierke's disease, which results in hyper uricemia and xanthoma formation, occurs due to the accumulation of this substance. Insulin acts as an inhibitor to GSK3 which phosphorylates an enzyme in its synthesis, while a unique enzyme necessary to its synthesize has a alpha-1,6 branch is simply called "branching enzyme." The protein involved in its synthesis has a tyr-194 residue with catalytic activity and forms an octa
Von Gierke's disease, which results in hyper uricemia and xanthoma formation, occurs due to the accumulation of this substance. Insulin acts as an inhibitor to GSK3 which phosphorylates an enzyme in its synthesis, while a unique enzyme necessary to its synthesize has a alpha-1,6 branch is simply called "branching enzyme." The protein involved in its synthesis has a tyr-194 residue with catalytic activity and forms an octamer by successive addition of UDP glucose molecules, and its breakdown sees the cleavage of a 1,4-alpha glycosidic bond. For 10 points, identify this polymer which is the form used for storing glucose in the liver.
Von Gierke's disease, which results in hyper uricemia and xanthoma formation, occurs due to the accumulation of this substance.
{glycogen}