It produces much of the cell's supply of ATP through oxidative phosphorylation.
Kearns-Sayre syndrome is a disease associated with malfunction of this organelle. Nonsyndromic deafness, ataxia, and neuropathies may result from mutations in this organelle's DNA, which is inherited entirely from the mother. The inner of this organelle's two membranes has compartments called (*) cristae and contains the matrix, which contains enzymes that oxidize pyruvate. It produces much of the cell's supply of ATP through oxidative phosphorylation. For 10 points, name this energy-generating organelle.
Kearns-Sayre syndrome is a disease associated with malfunction of this organelle.
{mitochondria} [or {mitochondrion}]