PEX5 and PEX7 are responsible for transport of enzymes to this organelle, which is disrupted in Zellweger's syndrome.
Defects in this organelle can lead to Pipecollic acidemia, while one enzyme here is responsible for processing of phytanic acid during myelin sheath formation. Mutations in its ABCD1 membrane transporter result in very long-chain fatty acid buildup in adrenoleukodystrophy, and this organelle is a secondary site for beta-oxidation. PEX5 and PEX7 are responsible for transport of enzymes to this organelle, which is disrupted in Zellweger's syndrome. The enzyme with the highest known turnover rate is found here, and this organelle is responsible for the breakdown of D-amino acids. Its primary function is carried out by Asn-147 and His-74 around porphyrin rings in the enzyme catalase. For 10 points, name this cellular structure responsible for breaking down hydrogen peroxide.
Defects in this organelle can lead to Pipecollic acidemia, while one enzyme here is responsible for processing of phytanic acid during myelin sheath formation.
{Peroxisomes}