Reye's syndrome can be caused by 3-mercaptoproprionic acid inhibiting an enzyme in this process, and a mutation in PCCA or PCCB inhibits one stage in this process.
Reye's syndrome can be caused by 3-mercaptoproprionic acid inhibiting an enzyme in this process, and a mutation in PCCA or PCCB inhibits one stage in this process. Another mutation affecting the transport of substrates for this process characteristically causes hypoketotic hypoglycemia, while another causes the buildup of dicarboxylic acids. Another defect in transport of substrates for this process is treated with Lorenzo's oil and is called adreno-leuko-dystrophy. It uses one molecule of both FAD and NAD per turn, and its final step per turn is catalyzed by beta-ketothiolase. The carnitine shuttle is used to transport substrates for this process, which takes place both in peroxisomes and mitochondria. Substrates with an odd number of carbons produce propionyl-CoA at the end of this process, which produces acetyl-CoA molecules from substrates like palmitate. FTP, name this process which breaks down fatty acids, and gets its name from the fact that it adds oxygen to the second carbon from the end.
Reye's syndrome can be caused by 3-mercaptoproprionic acid inhibiting an enzyme in this process, and a mutation in PCCA or PCCB inhibits one stage in this process.
Beta-oxidation