Although these patients have severe hypogammaglobulinemia and lymphopenia, the risk of infection is not very high and opportunistic infections are rare 6. There have been reports of meningitis and disseminated cryptococcal infections.
A pesar de que estos pacientes presentan hipogammaglobulinemia severa y linfopenia, el riesgo de contraer una infección no es muy elevado y las infecciones oportunistas son poco comunes 6.