The localized form involves skin lesions without visceral involvement. The systemic form is divided into a limited form called the CREST syndrome calcinosis, Raynaud phenomenon, esophagopathy, sclerodactyly and telangiectasia, a diffuse form and a visceral form without cutaneous involvement 2.
La forma localizada involucra lesiones de piel sin compromiso visceral y la forma sistémica se subdivide en forma limitada que incluye el síndrome CREST calcinosis, Raynaud, esofagopatia, esclerodactilia y telangiectasias, forma difusa y forma visceral sin compromiso cutáneo 2.