10.5826/dpc.1302a94
text/xml
2160-9381
2692
en
Sijia Chen
https://creativecommons.org/licenses/by-nc/4.0
Dermatology Practical & Conceptual
Juvenile Pityriasis Rubra Pilaris
Text.Serial.Journal
https://dpcj.org/index.php/dpc
Image Letter
2023-04-29
2022-07-07
2023-04-29
2023-06-05
e2023094
Dermatol Pract Concept
Sijia Chen
2023/04/29
10.5826/dpc.1302a94
e2023094
Traditional Chinese Medicine Hospital of Shangyu, Shaoxing, China
2160-9381
en
e2023094
Cohen PR, Prystowsky JH. Pityriasis rubra pilaris: a review of diagnosis and treatment. J Am Acad Dermatol. 1989;20(5 Pt 1):801-807. doi:10.1016/s0190-9622(89)70093-1.
Juvenile Pityriasis Rubra Pilaris
https://dpcj.org/index.php/dpc/article/download/2692/2088
                             Juvenile Pityriasis Rubra Pilaris
                                    Yihang Xie1, Lixia Xie1, Xin Shi2, Sijia Chen3


1 Chengdu Second People’s Hospital, Chengdu, China
2 The Second Affiliated Hospital of Soochow University, Suzhou, China
3 Traditional Chinese Medicine Hospital of Shangyu, Shaoxing, China



Citation: Xie Y, Xie L, Shi X, Chen S. Juvenile Pityriasis Rubra Pilaris. Dermatol Pract Concept. 2023;13(2):e2023094.
DOI: https://doi.org/10.5826/dpc.1302a94
Accepted: September 27, 2022; Published: April 2023
Copyright: ©2023 Xie et al. This is an open-access article distributed under the terms of the Creative Commons Attribution-
NonCommercial License (BY-NC-4.0), https://creativecommons.org/licenses/by-nc/4.0/, which permits unrestricted noncommercial use,
distribution, and reproduction in any medium, provided the original authors and source are credited.
Funding: None.
Competing interests: None.
Authorship: All authors have contributed significantly to this publication.
Corresponding author: Xin Shi, Department of Dermatovenereology, The Second Affiliated Hospital of Soochow University, 1055 Sanxiang
Street, Suzhou 215000, Jiangsu, China. E-mail: shx9@163.com




Case Presentation                                                        Teaching Point
A 4-year-old girl, without a prior history of eczema or psori-           Pityriasis rubra pilaris is a rare inflammatory skin disease that
asis, presented with a 4-weeks history of extensive erythem-             affects men and women of all ages, which presents with hy-
atous scaly eruption which started on her face and scalp,                perkeratotic follicular papules, erythematous-desquamative
and spread rapidly to her torso and limbs (Figure 1, A, B, E             plaques, palmoplantar keratoderma [1]. Its classification
and F). She also had well-circumscribed, red-orange, waxy                into five subgroups is based on age at onset, clinical course,
plaques on the palms and soles (Figure 1, C and D). Her                  morphologic features, and prognosis [2]. We present a type
growth and psychomotor development were normal. Histo-                   III pityriasis rubra pilaris. The differential diagnosis includes
pathology showed basket-like hyperkeratosis, diffuse ortho-              psoriasis vulgaris, perifollicular keratosis, lichen spinulosus.
keratosis and spotted parakeratosis, and a dermal superficial
perivascular lymphocytic infiltration (Figure 1G). The final
diagnosis was pityriasis rubra pilaris.




Image Letter | Dermatol Pract Concept. 2023;13(2):e2023094                                                                              1
Figure 1. (A,B,E,F) Extensive erythematous scaly eruption on the trunk and limbs. (C,D) Well-circumscribed, red-orange, waxy plaques
on the patient palms and soles. (G) Basket-like hyperkeratosis, diffuse orthokeratosis and spotted parakeratosis, and a dermal superficial
perivascular lymphocytic infiltration (H&E x400).



References                                                              2. Cohen PR, Prystowsky JH. Pityriasis rubra pilaris: a review
                                                                           of diagnosis and treatment. J Am Acad Dermatol. 1989;20
 1. Wang D, Chong VC, Chong WS, Oon HH. A Review on                        (5 Pt 1):801-807. DOI:10.1016/s0190-9622(89)70093-1. PMID:
    Pityriasis Rubra Pilaris. Am J Clin Dermatol. 2018;19(3):377-          2654219.
    390. DOI:10.1007/s40257-017-0338-1. PMID: 29302927.




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