10.5826/dpc.1302a108
text/xml
2160-9381
2779
en
Ramon Grimalt
https://creativecommons.org/licenses/by-nc/4.0
Dermatology Practical & Conceptual
A Midline Maxillary Tusk-Shaped Incisor in an Infant 
Text.Serial.Journal
https://dpcj.org/index.php/dpc
Image Letter
2023-04-29
2022-08-24
2023-04-29
2023-06-05
e2023108
Dermatol Pract Concept
Ramon Grimalt
2023/04/29
10.5826/dpc.1302a108
e2023108
Department of Dermatology, Universitat Internacional de Catalunya, Barcelona, Spain
2160-9381
en
e2023108
Garcia Rodriguez R, Garcia Cruz L, Novoa Medina Y, et al. The solitary median maxillary central incisor (SMMCI) syndrome: Associations, prenatal diagnosis, and outcomes. Prenat Diagn. 2019 May;39(6):415-419.
A Midline Maxillary Tusk-Shaped Incisor in an Infant 
https://dpcj.org/index.php/dpc/article/download/2779/2101
                 A Midline Maxillary Tusk-Shaped Incisor
                              in an Infant
      Mario Cutrone1, Vincenzo Piccolo2, Alejandro Ontiveros-Holguín3, Ramon Grimalt4


1 Department of Pediatric Dermatology, Ospedale dell’Angelo, Venice, Italy
2 Dermatology Unit, University of Campania Vanvitelli, Naples, Italy
3 School of Medicine, Universidad Autónoma de Durango Campus Chihuahua, Chihuahua, Mexico
4 Department of Dermatology, Universitat Internacional de Catalunya, Barcelona, Spain



Citation: Cutrone M, Piccolo V, Ontiveros-Holguín A, Grimalt R. A Midline Maxillary Tusk-Shaped Incisor in an Infant.
Dermatol Pract Concept. 2023;13(2):e2023108. DOI: https://doi.org/10.5826/dpc.1302a108
Accepted: September 21, 2022; Published: April 2023
Copyright: ©2023 Cutrone et al. This is an open-access article distributed under the terms of the Creative Commons
Attribution-NonCommercial License (BY-NC-4.0), https://creativecommons.org/licenses/by-nc/4.0/, which permits unrestricted
noncommercial use, distribution, and reproduction in any medium, provided the original authors and source are credited.
Funding: None.
Competing Interests: None.
Authorship: All authors have contributed significantly to this publication.
Corresponding Author: Vincenzo Piccolo, MD, c/o II Policlinico, Edificio 9, Primo piano, Via Pansini 5 - 80131 Napoli, Italy.
Tel: +39-0815666834 FAX: +39-0815468759 E-mail: piccolo.vincenzo@gmail.com




Case Presentation                                                        premature dentition with different structural characteristics
                                                                         than the transitional teeth that persist until the time of de-
A 4-month-old boy, who previously presented for a sizable                finitive dentition.
gingival hemangioma on the lower gingiva two months ear-                      Solitary median maxillary central incisor syndrome is a
lier and was being treated with propranolol and monthly                  mild manifestation of the holoprosencephaly spectrum, typ-
follow-up, now presented with a sudden onset of a white le-              ically exhibiting an eruption of normal morphology in the
sion in the upper gingiva that caused great discomfort during            midline of the maxillary alveolus at age of 8 months; pres-
breastfeeding to his mother one morning. Examination of                  ent in both primary and permanent dentition [1,2]. An ini-
the oral cavity revealed in the midline of the upper gingiva, a          tial head ultrasonography was performed with no anomaly
primary dental eruption reminiscent of a tusk or a fang due              being found.
to its incurved crown and sharp vertex (Figure 1A).                           Considering the absence of other malformative elements,
    While waiting dental and maxillofacial surgery consulta-             genetic evaluation was postponed to a later period of life.
tions, the lesion abruptly disappeared. A small central muco-            At age of 6 months, the boy developed an eruption of the
sal swelling with a slightly hemorrhagic pedicle at the site of          upper left canine and lower central incisor teeth of normal
detachment remained visible.                                             morphology (Figure 1B).

Teaching Point
                                                                         Acknowledgement: Patient parents in this manuscript has
Strictly speaking, this is not a neonatal tooth nor is it a na-          given written informed consent to the publication of her case
tal tooth. That said, its early decay suggests a somewhat                details.




Image Letter | Dermatol Pract Concept. 2023;13(2):e2023108                                                                           1
    Figure 1. (A) Tusk-shaped primary dental eruption in the midline of the upper gingiva at age 4 months. (B) Primary eruption of the upper
    left canine and lower central incisor teeth at age of 6 months.




References                                                                 2. Garcia Rodriguez R, Garcia Cruz L, Novoa Medina Y, et al.
                                                                              The solitary median maxillary central incisor (SMMCI) syn-
1. Hall RK. Solitary median maxillary central incisor (SMMCI)                 drome: Associations, prenatal diagnosis, and outcomes. Prenat
   syndrome. Orphanet J Rare Dis. 2006;1:12. DOI: 10.1186/1750                Diagn. 2019;39(6):415-419. DOI: 10.1002/pd.5451. PMID:
   -1172-1-12. PMID: 16722608. PMCID: PMC1464380.                             30900264.




2                                                                                Image Letter | Dermatol Pract Concept. 2023;13(2):e2023108
