Triple A syndrome (TAS  MIM #231550) or Allgrove’s syndrome is an autosomal recessive disorder  characterized by clinical triad of alacrima  adrenal insufficiency (AI) and achalasia cardia TAS patients may have varied neurological dysfunction (ND) in the form of distal sensory motor polyneuropathy  autonomic dysfunction  dementia  mental retardation  bulbospinal amyotrophy  optic atrophy  parkinsonian features  dysarthria  dystonia and chorea (1)